儿童间歇性肺部疾病:从波兰推中心的15年观察中吸取的教训
Honorata Marczak1, Katarzyna Krenke1, Katarzyna Solarska-Rydz1
1Department of Pediatric Pneumonology and Allergy, Medical University of Warsaw, Warsaw, Poland.
Pediatric pulmonology
|May 10, 2025
概括
儿童间歇性肺部疾病 (chILD) 是多种多样的,其中婴儿持续性气喘/婴儿神经内分泌细胞增生 (PTI/NEHI) 是最常见的. 大多数患有CHILD的儿童在治疗后出现改善或稳定.
科学领域:
- 儿科肺病学 儿科肺病学
- 罕见疾病 罕见疾病
- 间歇性肺部疾病 间歇性肺部疾病
背景情况:
- 儿童间歇性肺病 (chILD) 是一种罕见的慢性呼吸道疾病.
- 症状包括快速呼吸,呼吸短促,低氧和异常的肺部成像.
- 这些疾病在儿科护理中构成了诊断和管理的挑战.
研究的目的:
- 分析CHILD的原因,临床特征,治疗方法和结果.
- 在一个波兰儿科转诊中心,对CHILD的谱系进行了表征.
- 为了解决这些罕见的肺部疾病的管理提供见解.
主要方法:
- 对275名被诊断患有CHILD.的儿科患者 (0-18岁) 的回顾性审查.
- 在华沙医学大学从2009年6月到2024年2月收集的数据.
- 根据chILD-EU分类系统进行分类.
主要成果:
- 婴儿持续性气喘/婴儿神经内分泌细胞增生 (PTI/NEHI) 是最常见的诊断 (52.4%).
- 裂,呼吸不全和呼吸暂停是主要的症状.
- 超过92%的患者通过治疗得到改善或稳定,5年生存率为95.66%.
结论:
- 儿童包括各种各样的疾病,其中PTI/NEHI是最常见的.
- 有效的治疗策略在大多数儿科患者中带来了良好的结果.
- 需要进一步的研究来理解和管理未定义的chILD病例.
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