偶发的儿科宫内膜膜瘤:一个说明性的案例
Adriano M Lino-Filho1, Bárbara A Morais1,2, Mateus Neves Faria Fernandes3
1Division of Neurosurgery, Department of Surgery, Clinics Hospital, Federal University of Goiás, Goiânia, Goiás, Brazil.
Journal of neurosurgery. Case lessons
|May 19, 2025
概括
儿科宫内膜膜膜瘤是罕见的,经常被误诊的大脑瘤. 早期的手术干预可能是有益的,因为它们可能导致儿童的攻击性行为.
科学领域:
- 神经瘤学神经瘤学
- 儿科神经外科 儿科神经外科
背景情况:
- 脑膜瘤是常见的中枢神经系统瘤,但在儿童中很少出现 (0.4%-4.6%的儿科内瘤).
- 脑膜内膜瘤特别罕见,在儿科患者中经常被误诊为神经质神经瘤或洞穴瘤.
研究的目的:
- 突出诊断挑战和罕见的儿科宫内膜瘤的管理.
- 强调在儿科内轴内病变的差异诊断中考虑脑膜瘤的重要性.
主要方法:
- 一个4岁男孩的病例报告,偶然诊断出脑瘤.
- 使用MRI,光谱和 perfusion 成像进行初步评估.
- 通过手术后的病理和免疫组织化学分析确认了诊断.
主要成果:
- 在左舌环中发现了一个广的,异质的病变.
- 最初的成像表明,这是一个低度的质神经元瘤.
- 手术后的分析证实了纤维性脑膜瘤 (世卫组织1级).
结论:
- 脑膜内膜瘤很少见,在儿童中经常被误诊.
- 与成人相比,这些瘤在儿科患者中可能表现出更具侵略性的行为.
- 对于怀疑患有儿科宫内膜膜膜瘤的患者,通常建议进行手术.
相关概念视频
01:22Bacterial Meningitis I: Introduction
Bacterial meningitis is a severe, life-threatening inflammation of the meninges, particularly the pia mater and arachnoid mater, affecting the subarachnoid space, ventricles, and cerebrospinal fluid (CSF). If untreated, it can lead to significant neurological complications or death.Causative AgentsCommon pathogens vary with age and immune status. In adults, major organisms include Streptococcus pneumoniae, Neisseria meningitidis, and Haemophilus influenzae. Streptococcus agalactiae (group B...
01:26Brain Abscess l: Introduction
A brain abscess is a focal, intracerebral infection characterized by a localized collection of pus within the brain parenchyma, resulting from microbial invasion and the body’s inflammatory response. It progresses through stages: early and late cerebritis, followed by early and late capsule formation, reflecting tissue destruction, immune response, and eventual encapsulation.Etiology and PathogenesisCausative organisms vary with source and host factors, often involving polymicrobial infections,...
01:14Increased Intracranial Pressure l: Introduction
Intracranial hypertension is a sustained elevation of intracranial pressure (ICP) above 22 mm Hg. In supine adults, normal ICP is ~7–15 mm Hg.The rigid, nonexpandable cranium contains three components—brain tissue, blood, and cerebrospinal fluid (CSF)—that total ~1,700 mL in a typical adult: 1,400 mL brain (~80%), 150 mL blood (~10%), and 150 mL CSF (~10%). According to the Monro–Kellie doctrine, total intracranial volume is effectively fixed. When one component expands, CSF and venous blood...