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Updated: May 23, 2025

An In Vitro Model for the Study of Cellular Pathophysiology in Globoid Cell Leukodystrophy
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自性失调会在葡萄糖大脑糖酶缺乏症中触发先天性免疫激活

Magda L Atilano1, Alexander J Hull1, Kerri J Kinghorn1

  • 1Institute of Healthy Ageing, Department of Genetics, Evolution & Environment, University College London, London, United Kingdom.

Autophagy reports
|May 21, 2025
PubMed
概括

在高氏病 (Gaucher disease,GD) 中,自功能受损驱动肠道失调和免疫激活. 激活自,特别是在肠道,可能为GD提供治疗策略.

关键词:
在 GBA1 中,GBA1 是 GBA1 的代名词.戈舍氏病是戈舍氏病的一种疾病.帕金森病是帕金森氏症的一种疾病.自自是自的过程.葡萄糖大脑化酶的使用这是先天免疫力.这是一种 lysosomal lysosomal.

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