Rosa Lillo1,2, Maria Chiara Meucci1, Annamaria Del Franco3

  • 1Dipartimento di Scienze Cardiovascolari-CUORE Fondazione Policlinico Universitario A. Gemelli IRCCS Rome Italy.

概括

随着时间的推移,法布里病往往会使心脏损伤恶化,约有24%的患者表现出进展. 在法布里病中心脏参与恶化的关键预测因素包括年龄较大,男性性别,经典表型和功能衰竭.

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