系统性毛细血管泄漏综合征复杂的下肢腔综合征:一个病例报告
Asahi Ishihara1,2, Katsuyuki Sagishima1, Tadashi Ejima1
1Department of Critical Care Medicine, Kumamoto University Hospital, Kumamoto, Japan.
JA clinical reports
|June 9, 2025
概括
系统性毛细血管泄漏综合征 (SCLS) 可以导致严重的并发症,如隔间综合征. 这种罕见的疾病需要及时识别和管理,以减轻风险并改善患者的治疗结果.
科学领域:
- 内部医学 内部医学
- 血管生物学 血管生物学
- 罕见疾病 罕见疾病
背景情况:
- 系统毛细血管泄漏综合征 (SCLS) 是一种罕见的疾病.
- 它的特征是低血压,低albuminemia和血液度.
- 由增加的血管通透性和内皮功能障碍引起.
研究的目的:
- 报告一个罕见的SCLS病例.
- 为了突出SCLS复杂的双边下肢隔间综合征.
- 为了强调SCLS患者 compartment综合征的风险.
主要方法:
- 一个29岁的男性患者的病例报告.
- 诊断SCLS与单克隆性甘马病变 (IgG-λ).
- 治疗包括液体复苏,血管压缩剂,皮质类固醇和IVIG.
- 通过 Fasciotomy 进行双边下肢隔间综合征的管理.
主要成果:
- 患者出现了发烧,咳,鼻,低血压和.
- 严重的血液度 (Hgb 24.9 g/dL,Hct 69.3%) 和低蛋白血 (1.8 g/dL).
- 尽管初步接受了SCLS治疗,但发展了双边下肢隔间综合征.
- 在出院时用棍棒实现了行走.
结论:
- 分区综合征是SCLS的一个严重的潜在并发症.
- 早期识别和管理SCLS并发症至关重要.
- 这一案例强调了监测SCLS患者的隔间综合征的重要性.
相关概念视频
Assessment of the Cardiovascular System III: Palpation
1.6K
Palpation involves feeling the body to evaluate texture, size, consistency, and tenderness for assessing cardiovascular health. The following steps are organized in a head-to-toe order:
Jugular Venous Pressure (JVP) Measurement
Position the patient at a thirty- to forty-five-degree angle or in a semi-fowler's position. Look for the highest point of pulsation in the internal jugular vein and measure the vertical distance to the angle of Loius or sternal angle. A normal JVP is 3-4 cm above...
Jugular Venous Pressure (JVP) Measurement
Position the patient at a thirty- to forty-five-degree angle or in a semi-fowler's position. Look for the highest point of pulsation in the internal jugular vein and measure the vertical distance to the angle of Loius or sternal angle. A normal JVP is 3-4 cm above...
1.6K
Peripheral Arterial Disease II: Clinical Manifestations and Diagnostic Evaluation
764
Clinical manifestationsPeripheral Arterial Disease (PAD) manifests through a range of symptoms, from the characteristic intermittent claudication to atypical presentations and severe complications in advanced stages. Intermittent claudication, a hallmark symptom of PAD, presents as exercise-induced muscle pain that typically resolves within minutes of rest. This pain is reproducible and stems from inadequate blood flow, leading to the accumulation of lactic acid produced during anaerobic...
764
Peripheral Artery Disease IV: Nursing Management
702
The nursing management of a patient with peripheral artery disease (PAD) begins with a thorough assessment of the patient’s health history and clinical manifestations.AssessmentHealth History: Evaluate the patient’s history of hypertension, hyperlipidemia, family history of cardiovascular issues, and lifestyle factors such as dietary patterns, smoking, and physical activity.Physical Examination:Assess the affected extremity for decreased or absent peripheral pulses,...
702
Peripheral Artery Disease V: Postoperative Nursing Management
630
During the postoperative period, it is crucial to focus on maintaining circulation, identifying and managing potential complications, and planning for discharge.Nursing AssessmentVital signs monitoring: Regularly monitor vital signs, including blood pressure, heart rate, respiratory rate, and temperature, to detect early signs of complications such as bleeding and infection.Circulation assessment: Monitor pulses, perform Doppler assessments, and check capillary refill, color, temperature, and...
630
Venous Thrombosis IV: Nursing Management
415
Nursing management begins with a thorough assessment of the patient's health history. Key factors include trauma to veins, peripherally inserted central catheters, varicose veins, recent pregnancy or childbirth, surgery, bacteremia, prolonged bed rest, atrial fibrillation, COPD, heart failure, cancer, coagulation disorders, myocardial infarction, spinal cord injury, stroke, prolonged travel, recent bone fractures, and dehydration. Review medication intake, particularly oral contraceptives,...
415
Nephrotic Syndrome I : Introduction
1.2K
Nephrotic Syndrome is a chronic kidney disorder defined by clinical findings such as severe proteinuria, hypoalbuminemia, hyperlipidemia, and edema. These symptoms result from damage to the glomeruli, the kidney’s filtering units, increasing their permeability to proteins.Definition and Meaning:Proteinuria, defined as the loss of more than 3.5 grams of protein per day in adults, is a crucial feature of nephrotic syndrome. This condition is often accompanied by edema, the accumulation of...
1.2K


