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意大利为患有遗传代谢疾病的婴儿提供蛋白质替代品是否相同?

Margherita Di Costanzo1,2, Martina Tosi3,4, Martina Muzi5

  • 1Pediatrics and Neonatology Unit, Guglielmo da Saliceto Hospital, Piacenza, Italy.

Frontiers in nutrition
|June 10, 2025
PubMed
概括

对于遗传代谢疾病 (IMDs) 的婴儿蛋白质替代品 (PSs) 在营养含量上有所不同. 这项研究比较了意大利PS,发现一些具有高能量和必需脂肪酸但低微量营养素,突出了改善婴儿营养的领域.

关键词:
经典的同性囊性尿症.葡萄糖酸性尿尿症 1 型婴儿营养婴儿营养遗传代谢性疾病 遗传代谢性疾病糖 尿道疾病 尿道疾病有机酸emiaemia 是一种有机酸emia.蛋白质替代品 蛋白质替代品铁血症是什么意思

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