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Updated: Jun 13, 2025

Immunolabelling Myofiber Degeneration in Muscle Biopsies
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Published on: December 5, 2019

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早期内分体干扰和内分体通路功能障碍在杜恩肌肉发育不良症

Julie Chassagne1, Nathalie Da Silva1, Ines Akrouf1

  • 1Sorbonne Université, INSERM, Institute of Myology, Centre of Research in Myology, F-75013, Paris, France.

The American journal of pathology
|June 11, 2025
PubMed
概括

杜恩肌肉发育不良 (DMD) 涉及由于缺乏素而导致的内体细胞通路缺陷. 恢复营养不良或减少Rab5可以使这些缺陷正常化,为DMD提供新的治疗途径.

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