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Updated: Jun 13, 2025

Functional Reconstitution and Channel Activity Measurements of Purified Wildtype and Mutant CFTR Protein
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Published on: March 9, 2015

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CFTR突变导致囊性纤维化患者中性粒细胞内在功能障碍

Frank H Robledo-Avila, Raul Rascon, Alejandra Montanez-Barragan

    bioRxiv : the preprint server for biology
    |June 12, 2025
    PubMed
    概括

    囊性纤维化 (CF) 治疗方法,如ETI,通过纠正中性粒细胞中的CFTR蛋白来恢复中性粒细胞的抗菌功能. 这提高了杀死细菌的效果,并减少了CF患者的肺损伤.

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