脏血管肌脂瘤的谱与放射病学相关性
Meghan G Lubner1, Jamie Marko1, Myles T Taffel1
1From the Department of Radiology, University of Wisconsin School of Medicine and Public Health, Madison, Wis (M.G.L.); American College of Radiology Institute for Radiologic Pathology, 1100 Wayne Ave Suite 1020, Silver Spring, MD, 20910 (M.G.L., J.M., M.T.T., J.M.H.); Department of Radiology, NYU Langone Health, New York, NY (M.T.T.); Department of Radiology, Northwestern University Feinberg School of Medicine, Chicago, Ill (J.M.H.); and Department of Pathology, University of Michigan Medical School, Ann Arbor, Mich (A.M.U.).
血管肌脂瘤 (AML) 是一种由脂肪,肌肉和血管组成的良性瘤. 虽然AML通常是良性的,但可能会导致出血,并且可能需要根据大小和类型进行干预.
科学领域:
- 放射学 放射学是一门学科.
- 病理学 病理学 病理学
- 在瘤学瘤学.
背景情况:
- 血管肌脂瘤 (AML) 是一种介质瘤,其特征是血管,光滑肌肉和脂肪组织的混合.
- 美白细胞瘤与结核性硬化综合体 (TSC) 和淋巴管状菌瘤 (LAM) 有关.
- 对AML的成像发现与其病理组成相关,区分经典 (含脂肪) 和缺乏脂肪的变体.
研究的目的:
- 审查血管肌脂瘤的成像特征和临床行为.
- 讨论AML的组织病理特征和潜在并发症.
- 根据AML的呈现和风险因素概述当前的AML治疗策略.
主要方法:
- 对图像检测结果 (CT,MRI) 与基因病理学相关的审查.
- 对有关瘤行为,并发症和治疗结果的临床数据的分析.
- 图像特征与瘤组件 (脂肪,光滑肌肉) 的相关性.
主要成果:
- 缺乏脂肪的AML表现出特定的成像特征,如增加CT衰减和由于平滑肌肉占主导地位而导致的低T2信号.
- 出血是一种严重的并发症,特别是在大型AML或动脉瘤≥5毫米的患者中.
- 表皮性AML (EAML) 变种可能表现出侵略性行为,包括复发和转移.
结论:
- AML成像的外观对其组成和行为具有很高的预测性.
- 对AML的管理范围从观察到干预,根据病变特征和患者因素量身定制.
- 了解AML变体和潜在的并发症对于有效的临床管理至关重要.
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