在一个儿科患者中,右心室肌瘤伪装成血栓
Nikhila Rao1, Nilesh Rao1, George Alfieris2
1SUNY Upstate Medical University, Syracuse, New York, USA.
JACC. Case reports
|June 13, 2025
概括
儿科右心室肌瘤很少见,但可能导致肺栓塞. 通过心声学指导活检和手术切除进行早期诊断,导致完全康复.
科学领域:
- 儿童心脏病学 儿童心脏病学
- 心脏瘤学 心脏瘤学
- 诊断成像 诊断成像 诊断成像
背景情况:
- 初级心脏瘤在儿童中很罕见.
- 右心室 (RV) 肌瘤可以导致严重的并发症,如肺栓塞.
- 儿科肌瘤经常被误诊为其他心内质量.
研究的目的:
- 报告一个患有右心室髓瘤的儿科病人的病例.
- 突出诊断挑战和成功管理这种罕见的疾病.
- 强调在患有无法解释的症状的儿科患者中考虑myxoma的重要性.
主要方法:
- 一名十几岁的患者出现了胸痛和暗示肺栓塞的症状.
- 诊断得到证实,使用管回声心脏学引导的心内质量的活检.
- 右心室肌瘤经过手术切除.
主要成果:
- 该患者成功地通过手术切除右心室肌瘤进行治疗.
- 在术后实现了完全康复.
- 透导管活检在确立诊断方面是至关重要的.
结论:
- 右心室肌瘤在儿科患者中异常罕见.
- 及时诊断和手术干预对于有利的结果至关重要.
- 多模式成像和活检对于确定诊断至关重要,特别是在区分心内血栓和心内血栓时.
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