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Updated: Sep 18, 2025

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在溶酶体储存疾病中,溶酶血小板激活因子的二次积累

Pamela Kell1, Sonali Mishra1, Heather L Gray-Edwards2

  • 1Department of Medicine, Washington University School of Medicine, St. Louis, MO 63110, USA.

Molecular genetics and metabolism
|June 21, 2025
PubMed
概括

血小板激活因子 (lyso-PAFs) 被确定为各种 lysosomal存储疾病 (LSDs) 的二次存储化合物. 升高的lysos-PAF水平与疾病进展相关,并且在基因疗法下降,这表明它们可以用作生物标志物.

关键词:
病是病的一种疾病.柳索血小板激活因子的激活因子尼曼 - 皮克病A型桑德霍夫病是桑德霍夫病的一种疾病.泰·萨克斯病是泰·萨克斯病的一种疾病.

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