儿童中Forme Fruste胆固醇囊:临床表现和治疗结果-一项回顾性多中心研究
Aleksandar Sretenović1,2, Milan Slavković1, Dragana Vujović1,2
1Department of Pediatric Surgery, University Children's Hospital Belgrade, 11000 Belgrade, Serbia.
形成的胆固醇囊 (FFCC) 难以诊断,但通过胆道重建进行手术治疗是安全有效的. 在患有无法解释的胆道症状的儿童中,早期考虑对于预防并发症至关重要.
科学领域:
- 儿科手术 儿科手术
- 胃肠病学 胃肠病学
- 肝胆道手术 肝胆道手术
背景情况:
- 甲状腺胆固醇囊 (FFCC) 呈现出极少的肝外胆道扩张,通常在超声波上错过.
- FFCC与经典的胆固醇囊共同存在着炎症和恶性瘤的风险.
- 异常的胰腺胆道结 (APBJ) 经常与FFCC有关.
研究的目的:
- 介绍来自两个三级中心的儿科患者FFCC的管理经验.
- 评估FFCC手术治疗的临床成功和长期结果.
- 要突出考虑儿童患有无法解释的胆道症状的儿童患者的FFCC的重要性.
主要方法:
- 在2008年至2023年期间为FFCC治疗的儿科患者的回顾性分析.
- 临床成功的评估,以症状缓解和没有重大并发症来定义.
- 外科手术包括Roux-en-Y肝脏-jejunostomy或肝脏-双胞口与胆道重建的手术.
主要成果:
- 14名儿童接受了FFCC的手术治疗,平均年龄为5.3岁.
- 在13名患者中进行了Roux-en-Y肝脏-双关口术;其中一人有肝脏-双关口术.
- 在平均6.2年的随访期间,没有观察到胆管炎或静脉狭窄的病例;14.3%患有轻微的伤口感染.
结论:
- 由于微妙的成像和非特异性症状,FFCC带来了诊断挑战.
- 手术切除和胆道重建,通常是Roux-en-Y肝切除术,为FFCC提供安全有效的治疗方法.
- 对于儿科患者,无论管道扩张如何,在患有无法解释的胰腺炎或胆道问题时,积极考虑FFCC至关重要,以防止严重的并发症.
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