.

Katherine A Cheng1, Rose McNulty1, Holly Nichols1

  • 1From the Department of Radiology (K.A.C., R.M., H.N., H.P.M., T.S.H.), Department of Pathology (J.C.), and Division of Pulmonary, Allergy, and Critical Care Medicine (A.S.), Duke University Medical Center, 2301 Erwin Rd, Box 3808, Durham, NC 27710; Department of Radiology, Cincinnati Children's Hospital Medical Center, Cincinnati, Ohio (A.T., E.C.); and Department of Radiology and Biomedical Imaging, University of California San Francisco, San Francisco, Calif (M.V.).

概括

家族性肺纤维化 (FPF) 由于呈现变化和重叠的症状,存在诊断挑战. 与零星病例相比,早期诊断对于在FPF患者中获得更好的结果至关重要.

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