对德斯莫普拉金心肌病的诊断标准和疾病分期

Eric Smith1, Alessio Gasperetti2, Richard T Carrick2

  • 1Department of Internal Medicine, Division of Cardiovascular Medicine, University of Michigan, Ann Arbor, USA.

概括

对于Desmoplakin (DSP) 心肌病的新标准改善了诊断和风险分层. 这些基因特异性指导方针有助于识别患有心力衰竭和心律失常风险的患者,帮助未来的基因向治疗.

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