重组激活因子VIIa (NovoSeven) 治疗Glanzmann血栓塞的结果:两个病例报告
Eman Almatar1, Sondus Alsharidah, Omnia A Hashem
1Department of Hematology, NBK Specialized Children's Hospital, Kuwait.
概括
格兰兹曼血栓硬化 (GT) 是一种罕见的出血障碍. 重组激活因子VIIa (rFVIIa) 显示在管理GT出血和预防并发症方面具有前景,改善患者的生活质量.
科学领域:
- 血液学 血液学 血液学
- 血小板功能障碍 血小板功能障碍
- 血液静止 血液静止 血液静止
背景情况:
- 格兰兹曼血栓硬化 (GT) 是一种遗传性血小板疾病,由GPIIb/IIIa复合体的缺陷引起,导致粘膜皮肤出血.
- 目前的治疗方法,如血小板输血,存在与免疫接种和折射性相关的风险.
- 再组合激活因子VIIa (rFVIIa) 提供了一个替代的静血策略.
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