超膜大动脉狭窄模仿过度阻塞性心肌病:一个病例报告
Avneesh Sharma1, Emily Kaplan1, Yaqub Betz1
1Division of Cardiovascular Medicine, University of Virginia Health System, Charlottesville, VA 22902, USA.
超膜大动脉狭窄症可以模仿多变性心肌病,导致误诊. 多模式成像对于准确诊断和适当治疗左心室外流通道阻塞至关重要.
科学领域:
- 心脏病学 心脏病学
- 医疗成像医学成像
- 遗传学 遗传学 是一个
背景情况:
- 增高性心肌病变 (HCM) 是一种常见的遗传性疾病.
- 左心室外流管 (LVOT) 阻塞是HCM的常见并发症.
- 上大动脉狭窄 (SVAS) 可能出现类似的症状和成像发现,可能导致误诊.
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