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儿科大卫手术用于Loeys-Dietz综合征中动脉瘤扩张的上升大动脉
Pankaj Aggarwal1, Uday Tej Rajupalem1, Ramswaroop Sain1
1Department of Cardiothoracic and Vascular Surgery, Post Graduate Institute of Medical Education and Research, Chandigarh, India.
洛伊斯-迪茨综合征 (LDS) 需要为大动脉扩张进行手术修复. 一名患有LDS的3岁儿童成功接受了门节约性根部置换,保留了原生门,并显示出良好的恢复.
科学领域:
- 心血管外科心血管外科
- 遗传学 是一个遗传学.
- 儿童心脏病学 儿童心脏病学
背景情况:
- 洛伊斯-迪茨综合征 (LDS) 是一种罕见的遗传疾病,其特征是结缔组织异常.
- 上升大动脉的动脉扩张是LDS的常见和危及生命的表现,通常需要手术干预.
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