儿科大卫手术用于Loeys-Dietz综合征中动脉瘤扩张的上升大动脉

Pankaj Aggarwal1, Uday Tej Rajupalem1, Ramswaroop Sain1

  • 1Department of Cardiothoracic and Vascular Surgery, Post Graduate Institute of Medical Education and Research, Chandigarh, India.

概括

洛伊斯-迪茨综合征 (LDS) 需要为大动脉扩张进行手术修复. 一名患有LDS的3岁儿童成功接受了门节约性根部置换,保留了原生门,并显示出良好的恢复.