与IgG4相关的疾病呈现为中部头骨基骨质炎与深腹:一个病例报告
Shen-Han Lee1,2,3, Rohaizam Jaafar3, Nurul Akmar Misron4
1Department of Otorhinolaryngology-Head & Neck Surgery, School of Medical Sciences, Universiti Sains Malaysia, Health Campus, Kubang Kerian, Kelantan, Malaysia.
Medicine
|July 23, 2025
概括
这项案例研究揭示了IgG4相关的疾病 (IgG4-RD) 可以模仿感染,呈现为头骨基骨质炎和部. 早期考虑IgG4-RD对于耐火病例至关重要.
科学领域:
- 免疫学 免疫学 免疫学
- 耳鼻喉科 耳鼻喉科 耳鼻喉科
- 传染性疾病 传染性疾病
背景情况:
- 免疫球蛋白G4相关疾病 (IgG4-RD) 是一种全身性炎症性疾病.
- 它可以在头部和部表现出来,通常是类似瘤的质量.
- 本报告详细介绍了IgG4-RD.的新呈现方式.
研究的目的:
- 报告 IgG4 相关疾病的第一个病例,该病例呈现为中部头骨基骨质炎与深部.
- 突出IgG4-RD作为免疫抑制个体感染的潜在模仿.
- 强调在耐火性头骨底部感染中考虑IgG4-RD的重要性.
主要方法:
- 一个68岁的女性患有糖尿病,头痛,发烧和耳症状的病例报告.
- 诊断工作包括耳视镜,神经检查,鼻内镜,血液检查和成像 (揭示骨髓炎和).
- 一个深度活检的尾损伤证实IgG4相关的疾病.
主要成果:
- 患者最初通过抗生素和血糖控制得到改善,但后来出现了面部神经麻和听力损失.
- 对深病变的组织病理学检查证实了IgG4相关的疾病.
- 口服普雷迪尼索隆的治疗导致症状改善和瘤解脱.
结论:
- 中部骨基骨质炎与深部腹代表了IgG4-RD的新临床表现.
- IgG4-RD可能具有传染性特征,特别是在免疫功能低下的患者中.
- 组织活检对于诊断IgG4-RD在耐火性头骨骨底骨质炎和深部的情况下至关重要.
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