"没有检测到终点":一个独特的凝血概况揭示了纤维蛋白发育不良症
Kelsey Uminski1, Xiu Yan Jiang2
1Division of Hematology and Hematologic Malignancies, University of Calgary, Calgary, Alberta, Canada.
Case reports in hematology
|August 4, 2025
概括
纤维蛋白发育不良症是一种罕见的纤维素因子疾病,可导致出血或血栓形成. 及时的纤维素原替代对于诊断和治疗患者的诊断和管理至关重要,这些患者有不可解释的凝血测试.
科学领域:
- 血液学 血液学 血液学
- 遗传学 是一个遗传学.
背景情况:
- 纤维蛋白缺血症是一种罕见的纤维素素质性疾病.
- 它可以表现为出血,血栓形成或两者兼而有之.
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