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1Department of Pediatrics, The Ohio State University College of Medicine, Columbus, Ohio, USA.
针对囊性纤维化 (CF) 患者的新型简单的胸部CT评分系统显示出良好的可靠性,并准确地跟踪ETI治疗的疾病变化,与肺功能 (ppFEV1) 相对应良好. 这个系统简化了CF肺部评估.
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