焦点上的脆弱性:患有血管埃勒斯-丹洛斯综合征的患者的胆囊破裂
Sadhbh O'Connor1, Oscar Hocking2, Michael Warner1
1Hollywood Private Hospital, Perth, Australia.
ANZ journal of surgery
|August 15, 2025
概括
一个罕见的自发性胆囊出血病例导致血管埃勒斯-丹洛斯综合征 (vEDS) 患者的破裂. 这突出了在vEDS患者中严重的,以前未报告的胃肠道并发症.
科学领域:
- 胃肠病学 胃肠病学
- 血管外科 血管外科
- 遗传学 遗传学 是一个
背景情况:
- 埃勒斯-丹洛斯综合征 (EDS) 是一组遗传性结缔组织疾病.
- 血管EDS (vEDS) 是由于原缺乏导致的动脉和器官破裂的特征.
- 胆囊并发症通常与EDS无关.
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