对抗MDA5抗体阳性皮肤肌炎的临床和分子见解:单中心回顾性和转录性研究

Yunli Ren1, Tianqi Wu2, Weiwei Shi3,4

  • 1Department of Rheumatology and Immunology, Affiliated Hospital 2 of Nantong University, Nantong, People's Republic of China.

概括

抗MDA5抗体阳性皮肤肌炎 (MDA5-DM) 难以诊断,通常导致快速进展的间歇性肺病 (RP-ILD). 血清KL-6是MDA5-DM患者死亡率的关键预测因子.