优化ADAMTS13预防措施以减少先天性血栓性血栓性紫外线的复发和器官衰竭

Bérangère S Joly1, Adrien Joseph2, Raïda Bouzid3

  • 1Service d'Hématologie biologique, Hôpital Lariboisière, AP-HP. Nord, Université Paris Cité, Paris & INSERM UMRS1138, Centre de Recherche des Cordeliers, Université Paris Cité, Sorbonne Université, Paris, France, France.

Blood advances
|August 28, 2025
PubMed
概括

出生性血栓性血栓性紫外线 (cTTP) 需要进行密集的预防. 再组合ADAMTS13提供了一种安全有效的选择,改善了无复发的生存率并减少了长期的器官损伤.

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