一个重复的心脏瘤病例
Kurlya Yan1, Ashni Dharia1, Georgios Lygouris2
1Department of Internal Medicine, Allegheny General Hospital, Pittsburgh, Pennsylvania, USA.
JACC. Case reports
|August 29, 2025
概括
患有心脏复合体 (CNC) 的患者心脏肌瘤复发的风险显著增加. 终身监测对于治疗这种罕见的遗传疾病和预防心脏并发症至关重要.
科学领域:
- 心脏病学
- 遗传学
- 癌症学
背景情况:
- 角膜综合体 (CNC) 是一种罕见的遗传性疾病,与各种瘤有关,特别是心脏肌瘤.
- 由于潜在的栓塞事件,心律失常和心力衰竭,CNC患者的心肌瘤具有显著的死亡风险.
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