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Updated: Jan 18, 2026

Phosphorus-31 Magnetic Resonance Spectroscopy: A Tool for Measuring In Vivo Mitochondrial Oxidative Phosphorylation Capacity in Human Skeletal Muscle
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在先天性肌肉病的OXPHOS复杂缺陷:一个系统的审查

Megan J du Preez1, Maryke Schoonen1, Monray E Williams1

  • 1Mitochondria Research Group, Biomedical and Molecular Metabolism Research (BioMMet), North-West University, Potchefstroom, South Africa.

European journal of clinical investigation
|September 12, 2025
PubMed
概括

氧化酸化 (OXPHOS) 复杂功能障碍在先天性肌肉病中很常见,挑战其与线粒体疾病的排他性关联. 这一发现强调了线粒体参与作为先天性肌肉病理病理学的关键方面.

关键词:
出生性肌肉病变 (congenital myopathy) 是一种先天性肌肉病变.良好的健康和福祉.线粒体疾病是线粒体疾病.线粒体功能障碍 线粒体功能障碍神经肌肉疾病 诊断 诊断 神经肌肉疾病氧化酸化是一种氧化酸化.

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