在儿科年龄中与希尔施普朗格病相关的结肠卷发
Hazem Samir Amra1, Mostafa M Elghandour2, Mohammed Abdel-Latif3
1Pediatric Surgery Department, Faculty of Medicine, Ain Shams University, Cairo, Egypt. Hazem_samir@med.asu.edu.eg.
International journal of colorectal disease
|September 14, 2025
概括
儿童的结肠卷发 (CV) 很少见,但与赫尔施普朗格有关.
科学领域:
- 儿科手术 儿科手术
- 胃肠病学 胃肠病学
- 医学诊断 医学诊断 医学诊断
背景情况:
- 结肠卷发 (CV) 涉及结肠扭曲,这是儿童罕见但严重的疾病.
- 赫施普朗氏病 (Hirschsprung's disease,简称HD) 是儿科患者心血管病的已知危险因素,特别是在诊断延迟时.
研究的目的:
- 分析诊断为与希尔施普朗格病 (HD) 相关的结肠卷发 (CV) 的儿科患者的临床,放射学和管理数据.
- 突出儿童CV和HD之间的关联及其诊断影响.
主要方法:
- 进行了对医疗记录的回顾性审查.
- 该研究包括2000年1月至2022年12月期间被诊断患有CV和HD的儿科患者.
主要成果:
- 确定了21例儿科CV病例,其中42.9%与HD相关.
- 西格体卷发症是占主导地位的类型 (81%),通常与短段的HD有关.
- 在8例病例中,CV出现在HD诊断之前,表明潜在的诊断延迟或忽视.
结论:
- 在儿童中诊断结肠卷发症需要高度的怀疑指数.
- 在所有儿科CV病例中,必须考虑并排除赫施普朗格病,因为它与心血管疾病有显著的关联.
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