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Updated: Jan 17, 2026

Investigating von Willebrand Factor Pathophysiology Using a Flow Chamber Model of von Willebrand Factor-platelet String Formation
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在2A/IIC型威尔布兰德病中,通过外源性威尔布兰德病的补充来纠正VWF多元化

Ziqi Zhang1, Qian Liang1, Xiaoqian Xu2

  • 1Department of Laboratory Medicine, Ruijin Hospital, Shanghai Jiaotong University School of Medicine, Shanghai 200025, China; State Key Laboratory of Medical Genomics, Shanghai Institute of Hematology, Ruijin Hospital, Shanghai Jiaotong University School of Medicine, Shanghai 200025, China.

Molecular therapy : the journal of the American Society of Gene Therapy
|September 17, 2025
PubMed
概括

由于基因大小,对·维勒布兰德病 (VWD) 的基因治疗具有挑战性. 在2A/IIC型VWD模型中,在转化恢复的VWF多元化中补充VWF (VWFpp),提供一种新的治疗方法.

关键词:
基因治疗的基因疗法胺是一种胺.类型 2A/IIC 类型·威勒布兰德病是一种疾病.·威勒布兰德因素是什么

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