威尔基综合征:一种罕见的临床病例,表现为虚弱的白头
Marta Roldão1, Andreia Salgadinho Machado1,2, João Oliveira1
1Internal Medicine, Hospital de São Francisco Xavier, Lisbon, PRT.
Cureus
|September 19, 2025
概括
上层介质动脉综合征 (SMAS) 是一种罕见的胃肠道阻塞. 早期诊断和意识至关重要,特别是在无法解释的减肥患者中,以防止不良结果.
科学领域:
- 胃肠病学 胃肠病学
- 血管外科 血管外科
- 老年医学 老年医学
背景情况:
- 上层介质动脉综合征 (SMAS),也称为威尔基综合征,是一种罕见的疾病,导致胃肠道阻塞.
- 它是由于上层介质动脉和大动脉之间的十二指肠的压缩造成的,通常是在显著的体重减轻之后.
- 在年轻女性中,SMAS更常见,这使得老年患者的这种病例值得注意.
研究的目的:
- 报告一名92岁女性患者的SMAS病例.
- 突出SMAS的老年患者的诊断挑战和结果.
- 强调早期诊断的重要性和提高对SMAS的认识,特别是在经历不明原因减肥的患者中.
主要方法:
- 一个92岁的女性患者的案例研究,出现腹痛和吐.
- 使用计算机断层扫描 (CT) 诊断成像,以确定阻塞的原因.
- 实施保守的管理策略.
主要成果:
- 患者出现了符合胃肠道阻塞的症状,包括腹痛和吐,以及无法解释的体重减轻.
- 计算机断层扫描证实了高等关动脉综合征 (SMAS) 的诊断.
- 尽管采取了保守的措施,但患者的结果不利,导致死亡.
结论:
- 这一案例强调了早期诊断SMAS的必要性,即使在老年患者中也是如此.
- 提高对SMAS的临床意识是必不可少的,特别是在显著的不明原因体重减轻的个体中.
- 及时识别和管理对于改善患者的治疗结果和预防与SMAS相关的死亡率至关重要.
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