对患有·维勒布兰德病的患者进行麻醉管理:一个案例报告
Joshua Singavarapu1, Galina Borodulina2
1Anesthesiology, State University of New York Downstate Health Sciences University, Brooklyn, USA.
Cureus
|September 25, 2025
概括
本案例报告详细介绍了在接受割礼的婴儿中管理1型·威勒布兰德病 (vWD) 的方法. 特兰胺酸有效地控制了出血风险,确保了儿科患者的安全手术结果.
科学领域:
- 麻醉学 麻醉学
- 儿科手术 儿科手术
- 血液学 血液学 血液学
背景情况:
- ·威尔布兰德病 (vWD) 是一种影响血液静止的遗传性出血疾病.
- ·威尔布兰德因子 (vWF) 对血小板粘附和稳定第八因子至关重要.
- 1型vWD是最常见的形式,其特点是减少vWF水平.
研究的目的:
- 报告婴儿1型vWD的外科手术前管理情况.
- 为突出儿童患有出血障碍的儿科患者麻醉方面的考虑.
- 强调复杂案件的多学科团队协调.
主要方法:
- 一个病例报告,一个八个月大的男性患有1型vWD,接受了割礼.
- 术前评估和麻醉管理使用tranexamic acid.
- 监测生命体征和手术内/术后血静.
主要成果:
- 手术过程没有任何事件,生命体征稳定.
- 特兰胺酸有效地防止了显著的出血.
- 患者经历了一次短暂的喉发作,成功治疗.
- 没有观察到术后出血或出血并发症.
结论:
- 儿科患者的麻醉管理需要仔细的规划和监测.
- 特兰胺酸是一种可行的选择,用于管理vWD中的出血风险.
- 多学科合作对于优化患有出血障碍的儿科外科患者的术后护理至关重要.
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