一个年轻男孩的ALCAPA异常呈现:一个病例报告
1Department of Cardiovascular Surgery, West China Hospital Sichuan University, Chengdu, Sichuan, China.
Cardiology in the young
|September 29, 2025
概括
左主冠状动脉来自肺动脉的异常起源 (ALCAPA) 是一种罕见的缺陷. 肺高血压在一个孩子身上掩盖了ALCAPA,这给诊断带来了挑战,但手术取得了成功.
科学领域:
- 儿童心脏病学 儿童心脏病学
- 遗传性心血管缺陷 遗传性心血管缺陷
- 医疗成像医学成像
背景情况:
- 左主冠状动脉来自肺动脉的异常起源 (ALCAPA) 是儿童罕见的一种先天性心脏缺陷.
- 诊断通常包括通过血管学或心声学可视化异常起源或逆向流动.
- 肺高血压可以掩盖ALCAPA,提出诊断挑战.
研究的目的:
- 为了突出ALCAPA在幼儿中的诊断挑战.
- 提出一个肺高血压掩盖了异常冠状动脉起源的病例.
- 讨论手术纠正ALCAPA病例的管理和结果.
主要方法:
- 一个患有ALCAPA的儿科患者的病例报告.
- 诊断成像包括心声学和血管学.
- 涉及冠状动脉再植入和中枢门修复的手术干预.
主要成果:
- 心声图显示了非典型的特征,这是由于肺高血压的掩盖异常起源.
- 严重的 mitra 排泄被确定为二次肺高血压的原因.
- 成功的手术纠正导致显著的症状解决.
结论:
- 在有肺高血压的情况下,ALCAPA诊断可能具有挑战性.
- 严重的额头吐会导致肺高血压和非典型的ALCAPA呈现.
- 通过手术修复ALCAPA并修复心交,可以有效地缓解症状.
相关概念视频
Barrett Esophagus-II: Clinical Manifestations and Management
796
Individuals with Barrett's esophagus are often asymptomatic, but they may experience symptoms commonly associated with GERD, such as heartburn and acid regurgitation. Additional symptoms can include difficulty swallowing, chest pain, unintentional weight loss, blood in the stool (which may appear black, tarry, or bloody), and episodes of vomiting.
To diagnose Barrett's esophagus, healthcare providers often recommend an endoscopy for those showing symptoms of acid reflux. The procedure...
To diagnose Barrett's esophagus, healthcare providers often recommend an endoscopy for those showing symptoms of acid reflux. The procedure...
796
Aneurysm II: Clinical Manifestations and Diagnostic Studies
299
Thoracic, aortic arch and abdominal aneurysms are significant vascular conditions that can present with various clinical manifestations and lead to serious complications. Understanding these manifestations and the appropriate diagnostic studies is essential for effective management and treatment.Thoracic Aortic AneurysmsThoracic aortic aneurysms often remain asymptomatic until they reach a size that impinges on adjacent structures. They typically cause deep, diffuse chest pain that radiates to...
299
Peripheral Arterial Disease II: Clinical Manifestations and Diagnostic Evaluation
363
Clinical manifestationsPeripheral Arterial Disease (PAD) manifests through a range of symptoms, from the characteristic intermittent claudication to atypical presentations and severe complications in advanced stages. Intermittent claudication, a hallmark symptom of PAD, presents as exercise-induced muscle pain that typically resolves within minutes of rest. This pain is reproducible and stems from inadequate blood flow, leading to the accumulation of lactic acid produced during anaerobic...
363
Acute Pancreatitis I: Introduction
1.1K
Pancreatitis is inflammation of the pancreas, an organ located behind the stomach. It can be either acute or chronic.
Acute pancreatitis is characterized by rapid inflammation of the pancreas, often caused by factors like gallstone blockage or excessive alcohol consumption. Chronic pancreatitis, on the other hand, is a slow, progressive inflammation that may result from long-term alcohol abuse, obstructions in the pancreatic duct, or genetic factors.
The causes of acute pancreatitis include:
Acute pancreatitis is characterized by rapid inflammation of the pancreas, often caused by factors like gallstone blockage or excessive alcohol consumption. Chronic pancreatitis, on the other hand, is a slow, progressive inflammation that may result from long-term alcohol abuse, obstructions in the pancreatic duct, or genetic factors.
The causes of acute pancreatitis include:
1.1K
Acute Pancreatitis II: Clinical Manifestations and Management
756
Acute pancreatitis presents a complex medical emergency characterized by rapid onset inflammation of the pancreas, demanding timely diagnosis and management to prevent complications. The condition primarily manifests through severe upper abdominal pain that often radiates to the back. This pain intensifies following the consumption of fatty foods. Accompanying symptoms such as nausea, vomiting, abdominal distention, fever, dyspnea, cyanosis, and jaundice can vary in intensity but significantly...
756
Acute Pyelonephritis I: Introduction
493
Pyelonephritis is a bacterial infection that primarily affects the renal parenchyma and collecting system, including the renal pelvis, tubules, and interstitial tissue of one or both kidneys. It can be classified as either acute—a sudden, severe infection—or chronic, which refers to long-term or recurrent kidney infections.The primary cause of acute pyelonephritis (APN) is bacterial infection, with Escherichia coli accounting for approximately 70-80% of cases. Other bacteria, such...
493


