巨大的逆皮质单独神经纤维瘤
Katie Francine Lee1, Rathnayaka Mudiyanselage Kalpanee Dhanushika Gunasingha2, Jonathan Keung3
1General Surgery, Walter Reed National Military Medical Center, Bethesda, Maryland, USA katieflee22@gmail.com.
BMJ case reports
|October 9, 2025
概括
一个罕见的巨型逆肌神经纤维瘤病例,一种良性神经膜瘤,在一名年轻人身上被诊断出患有腹痛和腿部软弱. 手术切除导致了暂时的股骨神经麻,随后通过重建性手术和物理治疗恢复.
科学领域:
- 在瘤学瘤学.
- 神经学 神经学
- 手术病理学手术病理学
背景情况:
- 孤独的,良性逆上皮质神经纤维瘤是非常罕见的临床发现.
- 神经纤维瘤通常与遗传综合征有关,但可能偶尔发生.
研究的目的:
- 报告一例罕见的巨型单独的关节神经纤维瘤,起源于股骨神经.
- 讨论这种罕见瘤的诊断挑战,手术管理和术后结果.
主要方法:
- 一个年轻的男性患有腹痛和下肢神经缺陷的案例介绍.
- 诊断工作包括截面成像 (CT/MRI) 和组织活检.
- 在手术中切除了后质,随后进行了重建手术.
主要成果:
- 确定了一个大 (12.1 × 9.8 × 7.5厘米) 球状的,边缘很好的体质量,起源于左 iliopsoas 肌肉.
- 组织病理学分析证实了神经纤维瘤的诊断.
- 手术切除导致股骨神经麻,随着重建性手术和强化物理治疗,这种情况逐渐改善.
结论:
- 股骨神经外套的巨型单独逆肌神经纤维瘤非常罕见,即使在年轻患者中也是如此.
- 多学科的管理对于优化复杂的瘤患者的治疗结果至关重要.
- 早期诊断和适当的手术干预,随后进行康复,对于管理术后缺陷至关重要.
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