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Updated: May 7, 2026

Assay to Measure Nucleocytoplasmic Transport in Real Time within Motor Neuron-like NSC-34 Cells
08:53

Assay to Measure Nucleocytoplasmic Transport in Real Time within Motor Neuron-like NSC-34 Cells

Published on: May 16, 2017

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C9orf72 六核酸重复扩张损害了ALS中的微质反应

Pegah Masrori1,2,3, Baukje Bijnens4,5, Laura Fumagalli4,5

  • 1KU Leuven - University of Leuven, Department of Neurosciences, Laboratory of Neurobiology and Leuven Brain Institute (LBI), Leuven, Belgium. pegah.masrori@kuleuven.be.

Nature neuroscience
|October 14, 2025
PubMed
概括

零星ALS微质变得与疾病相关,而C9orf72ALS微质表现出减少的反应. 这揭示了ALS亚型中独特的细胞机制,影响了治疗策略.

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Real-Time Fluorescent Measurement of Synaptic Functions in Models of Amyotrophic Lateral Sclerosis

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