一个罕见的病例,一个复杂的冠状动脉三合体通过胸切除术在婴儿中得到修复
Tue Minh Vo1, Dung Duc Nguyen1, Hung Xuan Nguyen1
1Department of Thoracic and Cardiovascular Surgery, Hue Central Hospital, Hue, Vietnam.
JACC. Case reports
|November 3, 2025
概括
一种罕见的先天性心脏病,涉及冠状动脉动脉瘤和婴儿,通过早期手术成功治疗. 婴儿在右胸切除术后恢复良好,证明了这种方法的安全性和有效性.
科学领域:
- 儿童心脏病学 儿童心脏病学
- 遗传性心脏病是一种先天性心脏病.
- 血管外科 血管外科
背景情况:
- 冠状动脉动脉瘤 (CAA) 和涉及右冠状动脉 (RCA) 和鼻节动脉 (SNA) 排放到右心室的瘤是非常罕见的,以前的报道仅限于成年人.
- 这一案例是第一个在婴儿身上出现这种三位一体的案例.
研究的目的:
- 报告一个罕见的冠状动脉动脉瘤和婴儿的病例.
- 突出成功的手术管理和结果在儿科患者.
主要方法:
- 一个4个月大的婴儿有异常的右心房流量进行了计算机断层扫描,揭示了巨大的RCA和SNA动脉瘤与双胞胎进入右心房.
- 手术修复包括右下胸切除术,鼻节动脉 (SNA) 阻塞测试和绑定.
主要成果:
- 手术后的鼻节功能障碍自发地消失.
- 患者在第6天出院,一个月后仍然处于鼻节律,没有残留,有利于RCA动脉瘤回归.
结论:
- 在婴儿中,冠状动脉囊与巨型动脉瘤的三位一体,由于动脉瘤的大小和潜在的分流相关并发症,需要早期手术干预.
- 右胸切除术是婴儿右冠状动脉复杂异常的安全有效的手术方法.
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