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围脂在高氏病中的作用:系统性审查

Ashleigh Lake1,2, Maria Fuller3,4,5

  • 1Genetics and Molecular Pathology, SA Pathology at Women's and Children's Hospital, 72 King William Road, North Adelaide, 5006, Australia.

Orphanet journal of rare diseases
|November 6, 2025
PubMed
概括

氏病涉及脂积累,导致各种二次变化,如乳糖胺的升高和改变的化物. 了解这些细胞特异性脂形状是高氏病病理学的关键.

关键词:
改变了脂调节的调节.陶胺是一种陶胺.团结体 团结体 团结体 团结体戈舍氏病是戈舍氏病的一种疾病.肝炎复合性巨变症的发生乳糖胺酸是什么 乳糖胺酸是什么神经系统疾病 神经系统疾病皮肤异常 皮肤异常斯芬戈利皮德 de novo 合成斯芬戈脂类是指状的脂类.

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