带有胃肠道转移的桃体朗格汉斯细胞肉瘤:一个罕见的病例报告
Tahani Alanazi1, Leena Taher1, Hind Salama2,3
1Anatomical Pathology, National Guard Hospital, Riyadh, Saudi Arabia.
AME case reports
|November 10, 2025
概括
本案例研究详细介绍了一种来自桃体并扩散到胃肠道的侵袭性朗格汉斯细胞肉瘤 (LCS),该病例发生在一位老年女性身上. 这次罕见的演讲强调了管理先进的LCS与多器官参与的挑战.
科学领域:
- 在瘤学瘤学.
- 病理学 病理学 病理学
背景情况:
- 朗格汉斯细胞肉瘤 (LCS) 是一种罕见且具有攻击性的瘤.
- 带有胃肠道 (GI) 转移的桃体LCS异常罕见.
研究的目的:
- 报告一种罕见的带有广泛的胃肠道转移的桃体LCS病例.
- 描述临床表现,诊断发现和治疗过程.
主要方法:
- 桃体活检的组织学和免疫组织化学检查证实了LCS.
- 包括CT和PET-CT在内的成像研究被用于评估疾病的程度和进展.
- 治疗包括放射疗法和pembrolizumab,随后是息治疗.
主要成果:
- 一名83岁的女性出现了桃体LCS和随后的广泛的胃肠道转移.
- 患者经历了疾病的进展,尽管最初的治疗,导致胃肠道并发症,包括出血和穿孔.
- 患者的结果很差,诊断后六个月死亡.
结论:
- 这一案例凸显了LCS的攻击性和其潜在的异常转移模式.
- 针对LCS的向治疗和标准化管理协议需要进一步的研究.
- 更好地了解LCS病原和治疗对于更好的患者结果至关重要.
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