血清胆汁酸的升高预测了Alagille综合征儿童的肝脏不良结果:来自GALA研究小组的结果

Carla Fiorella Murillo Perez1, Shannon M Vandriel1, Emmanuel M Gonzales2

  • 1Division of Gastroenterology, Hepatology and Nutrition, The Hospital for Sick Children and the University of Toronto, Toronto, Canada.

概括

患有阿拉吉尔综合征 (ALGS) 的儿童的血清胆汁酸 (SBA) 水平较低,预测更好的肝病结果,包括本地肝存活率 (NLS) 和无事件存活率 (EFS). 这些发现表明,减少SBA可能会改善ALGS患者的临床结果.

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