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Updated: Jan 11, 2026

An Experimental System to Study Mechanotransduction in Fetal Lung Cells
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表面活性蛋白C成熟的不同途径,用于与疾病相关的异型

Sarah Bui1,2, Anamarie Reineberg1, Dakota Jones3,4

  • 1Pulmonary and Critical Care Division, Department of Medicine; Perelman School of Medicine at the University of Pennsylvania; Philadelphia, PA 19104.

bioRxiv : the preprint server for biology
|November 19, 2025
PubMed
概括

表面活性蛋白C (SP-C) 的突变破坏了其在肺细胞中的正常运输和加工,导致其在血膜上积累,而不是酸性LROs. 这种在多种模型中发现的改变途径涉及到由富林类蛋白转化酶损害的裂变.

关键词:
膜细胞2型细胞戈尔吉戈尔吉是一座古老的城市.蛋白转化酶的使用方法蛋白质成熟 蛋白质成熟表面活性蛋白C 表面活性蛋白C

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