婴儿瘤细胞上皮层癌:临床发现和成像特征
Patel Meet1, Maneesh Kumar Vijay2, Tarun Kumar Jain1
1Department of Nuclear Medicine.
Clinical nuclear medicine
|November 25, 2025
概括
这项研究报告了一例非常罕见的婴儿细胞上腺皮质癌病例. 早期诊断和手术切除是成功治疗这种儿科恶性瘤的关键.
科学领域:
- 儿科瘤学 儿科瘤学
- 内分泌学 在内分泌学.
- 病理学 病理学 病理学
背景情况:
- 儿科上腺皮质癌 (ACC) 是一种罕见的恶性瘤.
- 瘤细胞变异性ACC异常罕见,特别是在婴儿中.
- ACC可能表现为荷尔蒙过度活跃,例如雄激素水平升高.
研究的目的:
- 描述一个罕见的婴儿细胞上腺皮层癌的病例.
- 为突出这一罕见的儿科瘤的诊断和管理策略.
主要方法:
- 一名1岁女孩的病例报告显示,她有过度头发生长和声的症状.
- 激素评估显示雄激素水平升高.
- 使用全身18F FDG PET-CT进行诊断成像.
- 这是对上腺体的外科切除.
- 组织病理学确认和分级 (维尼克分数).
主要成果:
- 这位患者出现了雄激素过量的临床迹象.
- 图像检测发现了大量的左上腺质量.
- 组织病理学证实了细胞上腺皮质癌,具有高恶性瘤评分 (维尼克评分5).
- 患者经历了一次无事的术后康复.
结论:
- 瘤细胞上腺皮质癌是一种极其罕见的儿科恶性瘤.
- 多模式诊断方法对于及时诊断至关重要.
- 手术切除是主要的治疗方式.
- 手术后的管理包括激素替代和监测.
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