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Updated: Jan 9, 2026

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在CF亚群中肺部恶化风险的差异

D R VanDevanter1, C O'Rourke2, M W Konstan3

  • 1Case Western Reserve University School of Medicine, Cleveland, OH, USA.

Journal of cystic fibrosis : official journal of the European Cystic Fibrosis Society
|November 30, 2025
PubMed
概括

在患有囊性纤维化 (pwCF) 患者中,以前的肺恶化 (PEx) 强烈预测了未来的PEx风险,无论调节剂治疗如何. 即使使用elexacaftor/tezacaftor/ivacaftor (ETI),更高的先前PEx也表明未来风险更大.

关键词:
临床试验的设计前一年的事件频率.肺部恶化风险增加的风险

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