双手的状肌瘤与可能的头骨骨干涉:在成年人中极其罕见的情况
Mihaela Pertea1,2, Malek Benamor2, Alexandru-Hristo Amarandei3
1Surgery, Grigore T Popa University of Medicine and Pharmacy, Iași, ROU.
Cureus
|December 2, 2025
概括
多发性带病 (奥利埃病) 很少同时影响两只手. 这项研究强调了这种疾病的极度罕见性和对患者的心理影响,强调了需要支持的需要.
科学领域:
- 整形外科 整形外科 整形外科
- 医学遗传学 医学遗传学
- 在瘤学瘤学.
背景情况:
- 多发性带病 (奥利尔病) 是一种罕见的骨疾病.
- 典型的特征是状腺瘤,通常会影响长和平坦的骨头.
- 骨的干涉是非常罕见的.
研究的目的:
- 为了记录双边手参与奥利埃病的极度罕见情况.
- 报告同时出现不寻常和罕见的局部情况 (头,吐).
- 强调心理影响和需要患者支持.
主要方法:
- 从2015年到2025年进行系统的文献搜索 (PubMed,Scopus,谷歌学者).
- 关键词:奥利埃病, 染色体, 成人, 双手, 病例报告, 病例系列, 染色体瘤.
- 应用了包含/排除标准;数据系统地记录.
主要成果:
- 确认双边手参与奥利埃病的异常罕见.
- 在经过审查的文献中,只发现了五份此类报告.
- 在本综述中没有报告恶性转变 (冠状腺癌) 的病例.
结论:
- 有双边手部参与的奥利埃病非常罕见.
- 这种情况是衰弱的,治疗选择有限.
- 对于受影响的患者来说,心理和精神支持至关重要.
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