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Updated: Jan 9, 2026

Author Spotlight: Studying the Impact of Maternal Dietary Deficiencies on Long-Term Offspring Health Outcomes
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Author Spotlight: Studying the Impact of Maternal Dietary Deficiencies on Long-Term Offspring Health Outcomes

Published on: June 28, 2024

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在严重的甲基马龙酸和酸性酸性疾病中进行营养管理:有多少医疗食品是过多的?

Diane Margoses1, Apolline Imbard2,3,4, Clément Pontoizeau3,5,6

  • 1Reference Centre for Inborn Errors of Metabolism, Necker-Enfants Malades Hospital, APHP, Filière G2m, MetabERN, Paris, France.

Journal of inherited metabolic disease
|December 4, 2025
PubMed
概括

氨基酸混合物 (AAM) 可能通过改变血氨基酸水平,使甲基马龙酸血症 (MMA) 和酸血症 (PA) 患者的结果恶化. 建议优先考虑天然蛋白质摄入量,以更好地控制疾病.

关键词:
这就是MMA.在 PA PA PA 里面.低蛋白饮食是一种低蛋白饮食.医疗食品 医疗食品 是一种医疗食品.甲基马龙酸血症 甲基马龙酸血症有机酸性疾病有机酸性疾病有机酸性尿尿尿,有机酸性尿尿酸血症 酸血症

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