广泛的脑干损伤和宫肌病:克服一个严峻的预后 - 病例报告
Michaela Mencl1, František Charvát2, Radek Pádr3
1Department of Neurology, 2nd Faculty of Medicine, Charles University and Motol University Hospital, Prague, Czech Republic.
Case reports in neurology
|December 5, 2025
概括
脊柱V型持续性动脉静脉,与脊髓静脉排水的罕见形,可以导致渐进性骨髓病变. 一个案例突出了在诊断和成功的内血管治疗期间谨慎使用皮质类固醇的重要性.
科学领域:
- 神经学 神经学
- 血管外科 血管外科
- 放射学 放射学是一门学科.
背景情况:
- 冠状腺V型持续性动脉静脉囊是一种罕见的持续性动脉静脉瘤.
- 它们的特点是脊柱静脉排水进入周髓静脉.
- 在50%的病例中,这可能导致渐进性或上升性骨髓病变.
研究的目的:
- 为了呈现一种Cognard类型V管的病例.
- 为了强调在诊断不确定性时给予皮质类固醇时的谨慎.
- 为了突出成功的内血管治疗这种罕见的疾病.
主要方法:
- 一名59岁的男子出现了渐进的四肢和骨髓病变.
- 核磁共振扫描显示了大脑干和脊髓的广泛损伤.
- 传统血管学证实了持续的AVF;进行了内血管治疗.
主要成果:
- 皮质类固醇的使用使神经症状恶化.
- 传统的血管造影检测出一个持续的AVF.
- 最少侵入性内血管治疗是成功的.
结论:
- 冠状腺V型丸很少见,只有100例报告.
- 在不确定的诊断中,建议谨慎使用皮质类固醇.
- 内血管治疗提供了一个成功的治疗选择.
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