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Updated: Jan 9, 2026

One-step Metabolomics: Carbohydrates, Organic and Amino Acids Quantified in a Single Procedure
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从控制到优化:在蛋白质代谢的先天性错误的营养管理中发展战略

Júlio César Rocha1,2,3,4, Anne Daly5, Anita MacDonald5

  • 1Nutrition and Metabolism, NOVA Medical School (NMS), Faculdade de Ciências Médicas (FCM), Universidade Nova de Lisboa, Lisboa, Portugal.

Journal of inherited metabolic disease
|December 9, 2025
PubMed
概括

蛋白质代谢 (IEPM) 的先天性错误的营养管理需要进步. 营养治疗的未来创新,利用技术,旨在改善患者的生活质量和长期结果.

关键词:
在HCU中,HCU是指HCU.在MSUD中,MSUD是指MSUD.在PKU中,PKU是PKU.这就是TYRR.饮食 饮食 饮食 饮食营养状态 营养状况蛋白质蛋白质是蛋白质蛋白质的组成部分.限制的限制限制的限制.基板是一种基板.

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