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Updated: Jan 9, 2026

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线粒体铁素FDX2中的突变抑制了frataxin缺乏

Joshua D Meisel1,2,3,4,5, Pallavi R Joshi6,7,8,9, Amy N Spelbring10

  • 1Department of Molecular Biology, Massachusetts General Hospital, Boston, MA, USA. meisel@brandeis.edu.

Nature
|December 10, 2025
PubMed
概括

研究人员发现突变绕过了对铁硫合成的必要性. 降低FDX2水平显示了Friedreich治疗的潜力.

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