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Updated: Jan 8, 2026

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在家族性异形性肺纤维化中使用抗纤维治疗:一个比较队列研究

Keisuke Morikawa1, Yuzo Suzuki2, Shinpei Kato3

  • 1Second Division, Department of Internal Medicine, Hamamatsu University School of Medicine, Hamamatsu, Japan.

Scientific reports
|December 15, 2025
PubMed
概括

用抗纤维药物治疗的家族性肺纤维化 (FPF) 患者表现出与零星性异常性肺纤维化 (IPF) 患者相似的结果. 这项研究发现,在接受这些疗法的FPF-IPF患者中,死亡率或急性恶化风险没有增加.

关键词:
急性恶化是急性的恶化.抗纤维性治疗是一种抗纤维性治疗.家庭性肺纤维化异形性肺纤维化症 异形性肺纤维化症死亡率 死亡率 死亡率耐受性 耐受性

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