倾听力度及其与空间定位的关系,以及在阿舍尔综合征中的垂体和视觉障碍 - - 我们的经验
Tiziana Di Cesare1, Paola Michieletto2, Maria Teresa Bonati3
1Audiology and ENT, Institute for Maternal and Child Health-IRCCS "Burlo Garofolo", 34137 Trieste, Italy.
Audiology research
|December 24, 2025
概括
患有阿舍尔综合征 (USH) 的儿童经历了受听力损失和视觉/前体障碍影响的倾听努力. 空间意识,不仅仅是听力,影响疲劳,突出了需要知识博的教育工作者.
科学领域:
- 听力学 听力学是指听力学.
- 眼科医生 眼科 眼科
- 神经科学是一个神经科学.
- 遗传学 是一个遗传学.
背景情况:
- 听力损失 (HL) 的儿童经常经历显著的疲劳.
- 阿舍尔综合征 (USH) 结合了HL和视力障碍,可能会影响心理健康,社会情绪行为和学术人员.
- 了解USH的倾听努力对于支持受影响儿童至关重要.
研究的目的:
- 分析Usher综合征类型1和2的倾听力度.
- 研究听力努力与年龄,分子诊断,视力敏度,听力损失程度,前庭功能和空间定向等因素之间的关系.
主要方法:
- 一项对20名基因确诊的USH患者 (USH2:15,USH1:5),年龄在3-17岁之间进行的回顾性单心研究.
- 评估包括范德比尔特疲劳量表 (VFS),听力学/前体评估 (奥尔登堡矩阵,VHIT),声音定位测试和眼科检查.
- 数据分析将VFS得分与各种临床和听力学参数相关联.
主要成果:
- 与USH2.2相比,USH1患者表现出更明显的HL和较差的前庭功能.
- 在USH1和USH2之间的总体VFS得分没有显著差异,除了父母报告的身体疲劳.
- 听力努力 (VFS) 与年龄,听力值,听力设备使用,声音定位困难,VHIT不对称性,平衡问题和视野范围线性相关.
- 深度HL,有限的助听器使用,声音局部化不佳,平衡问题和视网膜敏感性低是倾听力度的风险因素.
结论:
- 在USH患者的倾听力度受到听力,前体和视觉功能的影响,影响空间意识.
- 环境因素,如学校环境,加剧了听力挑战.
- 教师需要提高对USH并发症的认识,以更好地支持学习并减少疲劳.
相关概念视频
Equilibrium and Balance
6.1K
The inner ear assumes dual functionalities of auditory perception and equilibrium maintenance. The vestibule is the organ responsible for balance. This organ contains mechanoreceptors, specifically hair cells, endowed with stereocilia, which aid in deciphering information regarding the position and motion of our heads. Two intrinsic components, the utricle and saccule, help perceive head position, while the semicircular canals track head movement. Neurological messages initiated in the...
6.1K
The Vestibular System
43.2K
The vestibular system is a set of inner ear structures that provide a sense of balance and spatial orientation. This system is comprised of structures within the labyrinth of the inner ear, including the cochlea and two otolith organs—the utricle and saccule. The labyrinth also contains three semicircular canals—superior, posterior, and horizontal—that are oriented on different planes.
43.2K
Perceiving Loudness, Pitch, and Location
885
The human brain perceives pitch through two primary mechanisms reflected in place theory and frequency theory. Each mechanism describes how sound waves are interpreted as specific pitches by the brain, offering insights into the intricate processes of auditory perception.
Place theory, or place coding, suggests that different pitches are heard because various sound waves activate specific locations along the cochlea's basilar membrane. The brain determines the pitch of a sound by...
Place theory, or place coding, suggests that different pitches are heard because various sound waves activate specific locations along the cochlea's basilar membrane. The brain determines the pitch of a sound by...
885
Auditory Perception
983
The auditory system is essential for sound perception, utilizing various critical structures. When sound waves enter the outer ear, they travel through the ear canal and cause the eardrum to vibrate. These vibrations are then transmitted to the middle ear, where three tiny bones – the malleus, incus, and stapes – amplify the sound. This amplification is crucial, as it ensures that the sound vibrations are strong enough to be conveyed to the inner ear. These vibrations then reach the...
983
Anatomy of the Ear
11.0K
Auditory sensation, commonly called hearing, involves the transformation of sonic waves into neural impulses facilitated by the structures of the auditory organ. The prominent, flesh-like structure on the side of the head, called the auricle, directs sound waves towards the auditory canal. The auricle is often mislabeled as the pinna, a term more aligned with mobile structures like a feline's external ear. The auditory canal penetrates the cranium via the external auditory meatus of the...
11.0K
Hearing
56.3K
When we hear a sound, our nervous system is detecting sound waves—pressure waves of mechanical energy traveling through a medium. The frequency of the wave is perceived as pitch, while the amplitude is perceived as loudness.
56.3K


