一个孤独的扩散型巨型神经纤维瘤由坐骨神经引起,发生在13岁的孩子身上:一种罕见的情况
Reshmi Sultana1, Suryadevara Sailaja2
1Department of General Surgery, Senior Resident, All India Institute of Medical Sciences, Bibinagar, Telangana 508126, India.
Oncoscience
|December 25, 2025
概括
坐骨神经的巨型孤独神经纤维瘤在儿童中很罕见. 这一案例突显了成功的手术切除和恢复,强调了精细的技术和手术内神经生理监测的潜在好处.
科学领域:
- 儿科手术 儿科手术
- 神经学 神经学
- 在瘤学瘤学.
背景情况:
- 深层外周神经的巨型孤独神经纤维瘤,特别是坐骨神经,在儿科患者中很罕见.
- 它们的深层肌肉间位置往往导致延迟诊断,直到显著的瘤生长.
研究的目的:
- 报告一个小儿病人的大坐骨神经神经纤维瘤病例.
- 讨论与这种罕见瘤相关的诊断和手术挑战.
- 强调手术技术和术后护理的重要性.
主要方法:
- 评估了一名13岁的男性,他有无痛的后大腿质量.
- 磁共振成像 (MRI) 确定了沿着坐骨神经的大型肌肉间质量.
- 瘤使用显微镜放大术切除了瘤,并仔细剖析了神经带.
- 组织病理学证实了扩散型细胞神经纤维瘤.
主要成果:
- 一个12.8厘米的肌肉间坐骨神经神经纤维瘤被成功切除.
- 患者在术后经历过一段暂时的脚下垂,这在物理治疗中得到缓解.
- 组织病理学证实了一种良性细胞神经纤维瘤,具有特定的免疫组织化学标记 (S100,SOX10,CD34,Ki-67).
结论:
- 细致的外科手术技术对于功能维护切除深层儿科神经纤维瘤至关重要.
- 术内神经生理监测 (IONM) 可能有助于神经的保存.
- 警的术后护理对于最佳的患者结果至关重要.
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