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Updated: Jan 7, 2026

Implementation of Non-invasive Point of Care Transient Elastography for Evaluation of Liver Disease in Pediatric Populations with Cystic Fibrosis
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在长期使用囊性纤维化跨膜行为调节器 (CFTR) 调节器的成年人中改善囊性纤维化相关的肝病

Sofia Manioudaki1, Larisa Vasilieva2, Eleni Geladari3

  • 1Intensive Care Unit, Sismanogleio General Hospital, 15126 Athens, Greece.

Life (Basel, Switzerland)
|December 30, 2025
PubMed
概括

长期使用囊性纤维化跨膜行为调节器 (CFTR) 调节器显著改善了CF成年人的肝病. 一半的患者在治疗后不再符合CF相关性肝病 (CFLD) 的标准.

关键词:
在CFTR调节器.成年人成年人成年人成年人成年人囊性纤维化症是什么囊性纤维化相关的肝脏疾病选择一个接收器/接收器/接收器/接收器.肝脏硬 肝脏硬 肝脏硬露卡弗托尔/伊瓦卡弗托尔是什么意思

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