围性结核甜症候群:一个病例报告和文献综述
Henry Bair1, Narmien Murdock1,2, Lara Cheslow3
1Oculoplastic and Orbital Surgery, Wills Eye Hospital, Philadelphia, Pennsylvania, U.S.A.
Ophthalmic plastic and reconstructive surgery
|December 31, 2025
概括
末性外围轨道甜蜜综合征模仿末性筋炎,但对皮质类固醇有反应,而不是抗生素. 早期活检和治疗可以揭示潜在的髓性白血病,并防止伤害.
科学领域:
- 皮肤病学 皮肤病学
- 血液学 血液学 血液学
- 在瘤学瘤学.
背景情况:
- 垂死周围轨道甜蜜综合征是一种不常见的疾病,可以被误认为是垂死膜炎.
- 这种错误诊断可能导致不适当的外科干预和延迟适当的治疗.
研究的目的:
- 为了突出死周围轨道斯威特综合征的独特临床表现和管理.
- 为了强调这种综合征与潜在的骨髓质恶性瘤之间的联系.
- 倡导早期活检和经验性皮质类固醇治疗.
主要方法:
- 一个60岁男性的病例报告,患有周围轨道亡.
- 检查诊断结果,包括CT,组织病理学和培养.
- 关于类似案例和管理策略的文献综合.
主要成果:
- 患者出现了眼皮胀,疼痛和死亡症,对抗生素没有反应.
- 组织病理学揭示了没有生物体的中性友皮肤病;培养是无菌的.
- 高剂量的皮质类固醇后出现了快速改善,揭示了潜在的急性髓性白血病.
结论:
- 垂死外围轨道甜蜜综合征需要一个不同的管理方法比垂死带炎.
- 在对抗生素无反应的无菌周围眼膜感染的情况下,考虑Sweet综合征.
- 早期诊断和用皮质类固醇治疗可以避免发病率,并发现隐藏的恶性瘤,如髓性白血病.
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