对于马凡综合征的眼部并发症的手术方法
Samuel A Cohen1, Meghana Kalavar1, Jayanth Sridhar2
1UCLA Stein Eye Institute, University of California Los Angeles, Los Angeles.
Current opinion in ophthalmology
|January 7, 2026
概括
手术的进步改善了马方综合征患者的视力,这些患者患有眼部并发症,如眼膜外和视网膜脱落. 然而,长期风险仍然存在,需要个性化手术规划和持续监测.
科学领域:
- 眼科医生 眼科 眼科
- 遗传学 是一个遗传学.
- 结合组织疾病 结合组织疾病
背景情况:
- 马方综合征是一种影响结合组织的遗传性疾病.
- 它经常导致视力威胁的眼部并发症.
- 这些病例包括长眼 (ectopia lentis),早期白内障,绿内障和视网膜脱落.
研究的目的:
- 为了回顾马凡综合征眼部并发症的最近的外科进展.
- 综合当前关于外科手术方法和结果的文献.
主要方法:
- 关于马凡综合征眼科手术的最新研究的文献综述.
- 对外,白内障,玻璃眼和视网膜脱落的手术技术的分析.
- 评估儿科和成人Marfan患者的结果和风险.
主要成果:
- 改善了ectopia lentis的技术 (例如,囊支装置,替代固定).
- 在儿科马芬患者中,视网膜脱落后透镜切除的风险更高.
- 通过现代的IOL公式提高了折射可预测性,但近视的进展仍在继续.
- 针对脆弱的眼睛进行量身定制的青光眼手术 (脑膜切除术,管道切换).
- 视网膜脱落的高终身风险,需要多次手术.
结论:
- 外科创新改善了马凡综合征患者的视觉结果.
- 显著的长期风险需要谨慎管理.
- 个性化手术策略,早期检测和长期随访至关重要.
相关概念视频
Angle Closure Glaucoma: Treatment
1.1K
Angle-closure glaucoma, or closed-angle glaucoma, is an eye condition where the iris bulges out and blocks the iridocorneal angle, resulting in a buildup of aqueous humor and increased intraocular pressure. Immediate medical attention is necessary due to the sudden onset of symptoms. The treatment for angle-closure glaucoma includes short-term and long-term approaches. Short-term treatment involves using eye drops like pilocarpine to lower intraocular pressure by increasing aqueous humor...
1.1K
Open Angle Glaucoma: Treatment
953
In open-angle glaucoma, the iridocorneal angle remains open, but the trabecular meshwork becomes stiff, slowing down the outflow of aqueous humor. This causes a buildup of aqueous humor in the anterior chamber, leading to a sudden increase in intraocular pressure. The treatment for open-angle glaucoma focuses on reducing the elevated intraocular pressure by either decreasing the secretion of aqueous humor or increasing its outflow.
Drugs such as carbonic anhydrase inhibitors, α2- and...
Drugs such as carbonic anhydrase inhibitors, α2- and...
953
Aneurysm III: Interprofessional Care
253
Aneurysm management involves either conservative medical therapy or surgical intervention, depending on the size and symptoms of the aneurysm. Conservative management is generally reserved for smaller, asymptomatic aneurysms, while larger or symptomatic aneurysms often necessitate surgical repair.Conservative Medical TherapyFor small, asymptomatic aneurysms, particularly abdominal aortic aneurysms (AAA) less than 5.5 centimeters in diameter, conservative medical therapy is recommended. This...
253


